 corticosteroid therapi amyloid nephrot syndrom treatment prolong adren corticosteroid 26 adult amyloid nephrot syndrom present subject observ seri 18 addit case summar literatur twenti-two patient male femal diagnosi establish renal biopsi 19 instanc autopsi 18 patient consid primari amyloidosi 8 secondari amyloidosi major subject di renal failur averag surviv onset diseas 17 6 month renal diseas indistinguish form nephrot syndrom except high incid purpur skin lesion low neglig incid hypertens time actual hypotens promin rapid inexor progress azotemia despit persist clinic biochem characterist nephrot syndrom amyloidosi percutan renal biopsi 12 cent 83 adult nephot syndrom corticosteroid appear affect progress diseas benefici detriment view high incid deleteri side effect prolong corticosteroid therapi avail potent diuret agent help reliev edema disord felt corticosteroid contraind treatment amyloid nephrot syndrom 